Skip to Content
Skip to Main Menu
Freephone Hearing Aid Advice
0800 567 7621
Book

Hereditary Hearing Loss: Causes, Signs and What Can Help

Kimberley Bradshaw - Head of Marketing
Written By:
Kimberley Bradshaw

Head of Online Medical Content

Paul Harrison - Audiology Expert at Hearing Aid UK
Audiologically Reviewed By:
Paul Harrison

Audiology Expert at Hearing Aid UK

Posted: 22nd July 2025
Updated and medically reviewed: 13th August 2026 in: Hearing Loss Awareness
FCC Image 2

What is Hereditary Hearing Loss?

What you need to know about the types, signs, treatments, and how to manage them

 

Overview     |    Types of hereditary hearing loss    |    How is hearing loss inherited?    |    What are the signs?    |    When to seek help    |     Treatment available    |    Living with hereditary hearing loss    |    Summary

 

Last Hearing Aid UK Update:  13

Overview

Most people lose some hearing as they get older, but for some, it happens much earlier, simply because of their genes. Hereditary hearing loss runs in families, caused by gene changes that make hearing get worse over time, sometimes gradually, sometimes quite suddenly.

If someone in your family struggles to hear, or you've been told you have hearing loss yourself, it's worth understanding the genetics behind it and what that might mean for you.

 

What is hereditary hearing loss?

Hereditary hearing loss comes down to a genetic change that affects the inner ear or the auditory nerve. Sometimes it's there from birth; other times it develops gradually. It can occasionally be linked to a wider syndrome, but more often than not, it shows up on its own with no other health conditions involved.

More often than not, the cause is a small change in the GJB2 gene, also known as connexin 26, which normally helps the inner ear make sense of sound. When it doesn't quite do its job, hearing loss can be there from the very beginning, or emerge quietly in the early years of childhood.

 

There are two types of hereditary hearing loss:

  • Non-syndromic hearing loss: By far the most common form, appearing on its own with no other health issues alongside it.
  • Syndromic hearing loss: Less common, and part of a broader picture, sometimes appearing together with other conditions such as vision or balance issues.

 

How is it inherited?

Autosomal dominant inheritance is when one parent carries the gene; each child faces a 50% chance of inheriting it. More often than not, it stays hidden until adulthood, when it finally starts to show.

Autosomal recessive works differently: both parents need to carry the gene for a child to be affected, and when that happens, hearing loss can be present from birth or develop early on.

The other two patterns are much rarer. X-linked inheritance is carried on the X chromosome and tends to affect men more than women. Mitochondrial inheritance, the rarest of all, is passed down only through the mother, though it can affect sons and daughters alike; mothers are the only ones who can pass it on.

 

Signs of hereditary hearing loss

  

When to see a doctor

If hearing loss runs in your family, it's worth keeping half an eye on your own hearing over the years, and having a word with your GP if anything changes.

Hearing loss that runs in families tends to develop gradually, but if you notice any sudden or significant changes, it's best to see a doctor without delay.

Getting your hearing checked early makes it easier to find what can help. An audiologist can help you figure out what's happening with your hearing and how significant it is. Your doctor will refer you to them for a hearing test.

Genetic testing may be recommended by your GP or a genetics specialist in some cases, to find out which genes are involved and how they work. This can help identify what might help, and, if you need them, the support services that are right for you.

 

What can help with hereditary hearing loss?

There's no cure for hereditary hearing loss, but there's a lot that can make everyday life easier:

  • Hearing aids make sounds louder and easier to follow in many different settings, and are fitted and fine-tuned in person by a qualified audiologist.
  • People with severe or profound hearing loss may be offered cochlear implants, which work around the damaged parts of the ear to stimulate the auditory nerve directly.
  • Speech therapy can help people who lose their hearing at a young age communicate more easily.

 

"Hereditary hearing loss is often misunderstood because people assume it only ever shows up in childhood. In reality, some gene changes don't cause noticeable changes until adulthood. If hearing loss runs in your family, it's worth getting your own hearing checked even if you feel fine, rather than waiting until it becomes obvious."

Paul Harrison, Audiology Expert & Founder, Hearing Aid UK

 

Living with hereditary hearing loss

Living with hereditary hearing loss has its challenges, but there's a lot that can make things easier. Support groups, online communities and your audiologist can all be a real source of help while you find your feet.

Everyday technology, from hearing aids to smartphones, can also make a big difference to how easily you communicate. In the UK, organisations like RNID offer helpful support and advice for people and families affected by hereditary hearing loss.

 

Summary

Hereditary hearing loss is more common than most people realise, and it can show up anywhere along the family tree, not just in the generation you'd expect. Understanding how it's passed down takes away a lot of the mystery, and getting your hearing checked sooner rather than later just makes everything that follows a bit easier.

People with hereditary hearing loss can still live full lives with the right support, thanks to better hearing aids, cochlear implants, and other audiologist-led care.

If you think you might have hereditary hearing loss, make an appointment with your GP. They'll refer you to an audiologist for a full hearing test and clear, independent advice on what can help.

 

Thinking hereditary hearing loss might run in your family?

If hearing loss runs in your family, or you've noticed changes in your own hearing, a good first step is speaking to your GP, who can refer you for a full hearing test.

Once you have that referral, our HCPC-registered audiologists offer a free hearing test, either at one of our 93+ clinics or during a free home visit, whichever suits you best. There's no obligation and no pressure, just clear, independent advice on what can help.

We're also Which? recommended, and trusted by over 31,000 customers across the UK. Call our team free on 0800 567 7621, or book online below.

Why Choose Us?

  • FREE Hearing Tests
  • Best Hearing Aids and Prices
  • FREE Aftercare for Life
  • FREE Home Visits
  • FREE Clinic Appointments
  • 200+ Local Audiologists
  • 60 Day Money Back Guarantee
Paul Harrison
Hearing Aid Advisor
Unlike most national retailers we are not owned by any manufacturer, this means we can offer the full choice of all makes and models of hearing aids

Do you think you might be losing your hearing?

If hearing loss runs in your family, or you've noticed changes in your own hearing, it's worth having a chat with your GP.

Getting checked early, and understanding a bit more about what's going on, can make a real difference to how you manage day to day.

Your GP can refer you to an audiologist for a full hearing test and honest advice on what can help.

With the right support, there's no reason hearing loss needs to hold you back.

Call 0800 567 7621
- or -
We Can Call You
Request a Callback
A friendly member of our team will call you back.
Or We Can Call You
Please correct any validation errors.
* Unsubscribe at any time. See our Privacy Policy
protected by Badge reCAPTCHA
Written by Kimberley Bradshaw

Meet Kimberley Bradshaw, Head of Online Medical Content

Kimberley Bradshaw is Head of Online Medical Content at Hearing Aid UK, with six years of experience writing about hearing healthcare for UK and US health and wellness publications. Her focus has always been the same: making complex topics feel clear, human, and easy to understand.

✔️ Head of Online Medical Content, Hearing Aid UK

✔️ Medical Content Writer — UK & US publications

✔️ 6 years experience writing in the audiology space

✔️ Member of Tinnitus UK

Audiologically reviewed by Paul Harrison

Meet Paul Harrison, Audiology Expert at Hearing Aid UK

Paul Harrison is an audiology expert at Hearing Aid UK, with over 20 years of experience helping people understand their hearing health and find the right solutions for their needs. He is committed to making audiological advice accessible, honest, and straightforward for everyone.

✔️  Council Member, BSHAA — 2015–2020

✔️  Audiology Expert, Hearing Aid UK

✔️ 20 years of audiology experience

Other hearing loss articles you might like...

What is a Cholesteatoma? What is a Cholesteatoma?
Persistent ear discharge, one-sided hearing loss or a feeling of fullness could point to a cholesteatoma, a rare but treatable build-up of skin cells behind the eardrum. Here's what causes it, what th...
Read More
I need subtitles all the time I need subtitles all the time
Why do subtitles help more than turning the volume up? For many people, needing them for everything, even English-language TV, is an early sign of hearing loss. Here's what's really going on.
Read More
Struggling to hear on public transport Struggling to hear on public transport
Stopped taking the bus or train because you can't quite keep up with announcements or conversations? You're not alone, and it could be more than just a preference. Find out what RNID's research says,...
Read More
Total Number of Happy Customers

31041
Established Over 10 Years
Reviews.io
Rated: Excellent
Unbiased Hearing Aid Advice You Can Trust

Our specialist service includes:

Free Independent, Impartial Advice
Free Aftercare for Life
Competitive Prices & National Support
60 day Money Back Guarantee - Risk Free
Over 200 Audiologists across the UK

Do not spend hundreds of pounds without getting a second opinion from us.

Please call us on 0800 567 7621

Quote Marks Not only are the prices great, but the service is fantastic! Many thanks to your team.
Jenny Smith - London
Verified Customer
reviews.io logo

What's included in our hearing aid prices?

Full Hearing Test & Examination by a Registered Audiologist
Fitting and Programming of Hearing Aid(s)
All Aftercare and Fine Tuning for Life
Full Manufacturer's Warranty
60 Day Full Money Back Guarantee

Watch the hereditary hearing loss video below

FAQs

What is the best hearing aid model for me?

In general, any audiologist will always recommend to you the hearing aid model that best suits your needs. Here is a useful checklist to make sure that is the case.

  • Audiologist's level of knowledge: The audiologist you have seen will hopefully have a wide knowledge of all available hearing aids; however, some will only be familiar with a small number of brands and, therefore, may not really be in a position to know which model is the best for you. It is OK to challenge their recommendation and ask them to justify why this particular brand is the one for you.
  • Do research: Read about the hearing aid that was recommended. Does it seem like it will suit your lifestyle? Does it have more or fewer features than you need? 
  • Be aware of sales targets: Many high street retailers have specific tie-ins to a particular manufacturer/brand. The hearing aid they have suggested may still be the correct one for you, but do your research so that you know why they might have recommended it.  You can read our best hearing aids of this year here
Do I need one hearing aid or two?

If you have significant hearing loss in both ears, you should be wearing two hearing aids. Here are the audiological reasons why:

Localisation: The brain decodes information from both ears and compares and contrasts them. By analysing the minuscule time delays as well as the difference in the loudness of each sound reaching the ears, the person is able to accurately locate a sound source. 

Simply put, if you have better hearing on one side than the other, you can't accurately tell what direction sounds are coming from.

Less amplification is required: A phenomenon known as “binaural summation” means that the hearing aids can be set at a lower and more natural volume setting than if you wore only one hearing aid.

Head shadow effect: High frequencies, the part of your hearing that gives clarity and meaning to speech sounds, cannot bend around your head. Only low frequencies can. Therefore, if someone is talking on your unaided side, you are likely to hear that they are speaking, but be unable to tell what they have said.

Noise reduction: The brain has its own built-in noise reduction, which is only really effective when it is receiving information from both ears. If only one ear is aided, even with the best hearing aid in the world, it will be difficult for you to hear in background noise as your brain is trying to retain all of the sounds (including background noise) rather than filtering them out.

Sound quality: We are designed to hear in stereo. Only hearing from one side sounds a lot less natural to us.

Fancy some further reading on this topic?  You can read about why two hearing aids are better than one in our article, hearing aids for Both Ears, here

What are the benefits of rechargeable hearing aids?

For most people, the main benefit of a rechargeable hearing aid is simple convenience. We are used to plugging in our phones and other devices overnight for them to charge up.  Here are some other pros and cons:

For anybody with poor dexterity or issues with their fingers, having a rechargeable aid makes a huge difference, as normal hearing aid batteries are quite small and some people find them fiddly to change.

One downside is that if you forget to charge your hearing aid, then it is a problem that can't be instantly fixed. For most, a 30-minute charge will get you at least two or three hours of hearing, but if you are the type of person who is likely to forget to plug them in regularly, then you're probably better off with standard batteries.

Rechargeable aids are also a little bit bigger and are only available in Behind-the-Ear models.

Finally, just like with a mobile phone, the amount of charge you get on day one is not going to be the same as you get a few years down the line. Be sure to ask what the policy is with the manufacturer's warranty when it comes to replacing the battery.

Are Behind-the-Ear hearing aids better than In-the-Ear hearing aids?

For most people, the answer is yes. But it's never that simple.

The majority of hearing problems affect the high frequencies a lot more than the low ones. Therefore, open fitting hearing aids sound a lot more natural and ones that block your ears up can make your own voice sound like you are talking with your head in a bucket. Therefore, in-ear aids tend to be less natural.

However, the true answer is we can't tell until we have had a look in your ears to assess the size of your ear canal, and until we have tested your hearing to see which frequencies are being affected.

People with wider ear canals tend to have more flexibility, also there are open fitting modular CIC hearing aids now that do not block your ears.

There is also the age-old rule to consider, that a hearing aid will not help you if it's sat in the drawer gathering dust. If the only hearing aid you would be happy wearing is one that people can't see, then that's what you should get.

Most people can adapt to any type of hearing aid, as long as they know what to expect. Have an honest conversation with your audiologist as to what your needs are.

What are channels, and how many do I need?

Generally speaking, six or more. Unless it's none at all.  The number of channels a hearing aid has is often a simplistic way an audiologist will use to explain why one hearing aid is better than another, but channels are complex, and it is really not that straightforward.  Here are some reasons why:

Hearing aids amplify sounds of different frequencies by different amounts. Most people have lost more high frequencies than low, and therefore need more amplification in the high frequencies. The range of sounds you hear is split into frequency bands or channels, and the hearing aids are set to provide the right amount of hearing at each frequency level.

Less than six channels, and this cannot be done with much accuracy, so six is the magic number. However, a six-channel aid is typically very basic with few other features and is suitable only for hearing a single speaker in a quiet room. The number of channels is not what you should be looking at; it's more the rest of the technology that comes with them.

As a final note, different manufacturers have different approaches. One method is not necessarily better than any other. For example, some manufacturers have as many as 64 channels in their top aids. Most tend to have between 17 and 20. One manufacturer has no channels at all.

What's covered in a manufacturer's warranty?​

Manufacturer's warranties typically last between 2-5 years, depending on the brand and model, and cover defects in materials and workmanship. This includes repairs for component failures, electronic malfunctions, and manufacturing defects, but excludes damage from misuse, accidents, or normal wear. Most manufacturers also include loss and damage insurance for the first year.

We handle all warranty claims on your behalf, liaising with manufacturers and ensuring you get replacement devices quickly when needed. This comprehensive warranty coverage, combined with our lifetime aftercare, gives you complete peace of mind.  Find out more about our warranty cover here

How much does the hearing test cost?

Our hearing tests are completely free, whether at our clinics or in your home. Unlike other providers who charge £30-£100 for home visits, we believe hearing healthcare should be accessible without financial barriers. Our comprehensive assessments include examination by an HCPC-registered audiologist, audiogram results, and personalised recommendations.

All testing, future adjustments, and ongoing support are included at no extra cost. While NHS tests are also free, typical 6-week waiting periods often lead people to seek immediate private testing. We provide prompt, professional assessments that fit your schedule and budget.

Do you offer home visits, and are they included in the price?

Yes, we offer completely free home visits throughout the UK, and this service is included in our prices with no additional charges. Home visits are particularly valuable for people with mobility issues, busy schedules, or those who simply prefer the comfort and convenience of their own environment.

Our audiologists can conduct full hearing tests, fit hearing aids, and provide ongoing support in your home.  This service sets us apart from many providers who either don't offer home visits or charge extra for them.

Why are your hearing aids cheaper than what I'd pay on the high street?

We can offer prices up to 40% lower than high street retailers because of our business model. As a network of 200+ independent audiologists, we don't have the massive overheads of large retail chains - no expensive high street premises, no sales targets pushing audiologists to sell the most expensive options, and no costly marketing campaigns.

However, we maintain the same buying power as the big chains because we purchase on behalf of our entire nationwide network. This means you get access to the same premium hearing aids with professional service, but at genuinely competitive prices.

How long do I have to try the hearing aids before committing to keep them?

We offer a comprehensive 60-day money-back guarantee, which gives you twice the industry standard time to properly assess whether your hearing aids are right for you. This extended period recognises that adjusting to hearing aids takes time, and your brain needs several weeks to adapt to the amplified sounds.

Unlike many providers who offer just 30 days, we believe 60 days gives you the confidence to test your hearing aids in all the situations that matter to you - from quiet conversations at home to busy restaurants and outdoor activities.

Other pages you might find useful

Audiology Home Visits - For free in the UK
View Audiology Home Visits - For free in the UK
Best hearing aids available in the UK for 2026
View Best hearing aids available in the UK for 2026
Hearing Tests at Home in the UK for free
View Hearing Tests at Home in the UK for free
Need advice? Give our hearing aid experts a call for FREE

Ask the Experts

Please correct any validation errors.

Get free independent impartial advice from the experts you can trust. We offer nationwide coverage and huge savings on all our hearing aids.

Hearing Aid UK Ltd.
6 Morton Lane
Walkwood
Redditch
Worcestershire
B97 5QA
Download Free Guide calendar logo Book a Free Appointment

Thank you, we have added you to our newsletter list.

© Hearing Aid UK Ltd. 2026

Latest Launch

When we refer to a product as 'Latest Launch', we mean it is the latest to be released on the market.

Close

New

When we refer to a product as 'New', we mean that the product is the newest hearing aid model on the market.

Close
Superseded

When we refer to a product as 'Superseded', we mean that there is a newer range available which replaces and improves on this product.

Close

Older Model

When we refer to a product as an 'Older Model', we mean that it is has been superseded by at least two more recent hearing aid ranges.

Close